Macrophage Activation Syndrome in a Child with Systemic Juvenile Rheumatoid Arthritis
Kerbala Journal of Medicine,
2007, Volume 1, Issue 1, Pages 170-173
AbstractMacrophage activation syndrome (MAS) is a rare and potentially fatal complication of rheumatic
disorders in children; we describe a 14-month old boy in whom MAS developed as first presentation of
systemic juvenile rheumatoid arthritis (S-JRA). He suffered from fever, bleeding tendency from mouth,
gastro-intestinal tract, ecchymosis & site of injections followed by bilateral wrist swellings. Physical
examination revealed cervical lymphadenopathy & hepatosplenomegaly. Laboratory findings were
abnormal liver enzymes, coagulopathies resembling disseminated intravascular coagulation, anemia,
thrombocytopenia and abnormal C.S.F. findings.
Up to the best of my knowledge this could be the first MAS associated with S-JRA in Iraq.
Key words: Macrophage Activation Syndrome, Arthritis, Juvenile Rheumatoid
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